Clicking on any metabolite link will take you to the Human Metabolome Database.
Displaying diseases 133 - 136 of 172 in total
Nonketotic Hyperglycinemia
MetaboliteConcentration in CSFPatient StatusAgeSexReferenceDetails
2-Ketoglutarate dehydrogenase complex deficiency  (203740 )
MetaboliteConcentration in CSFPatient StatusAgeSexReferenceDetails
Oxoglutaric acid (HMDB0000208) 101.0 (50.0-152.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both
  • MetaGene: Metabol...
details
Oxoglutaric acid (HMDB0000208) 875.0 (150.0-1600.0) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
Fumaric acid (HMDB0000134) 17-124 umol/mmol creatinineAbnormalInfant (0-1 year old)Male details
Malic acid (HMDB0000156) 7-194 umol/mmol creatinineAbnormalInfant (0-1 year old)Male details
Oxoglutaric acid (HMDB0000208) 30-1600 umol/mmol creatinineAbnormalInfant (0-1 year old)Male details
Succinic acid (HMDB0000254) 75-185 umol/mmol creatinineAbnormalInfant (0-1 year old)Male details
3-Phosphoglycerate dehydrogenase deficiency  (601815 )
MetaboliteConcentration in CSFPatient StatusAgeSexReferenceDetails
Adenosine kinase deficiency  (614300 )
MetaboliteConcentration in CSFPatient StatusAgeSexReferenceDetails
Adenosine (HMDB0000050) 7.1 umol/mmol creatinineAbnormalAdult (>18 years old)Male details
Adenosine (HMDB0000050) 9.9 umol/mmol creatinineAbnormalAdolescent (13-18 years old)Female details
Xanthine (HMDB0000292) 4.9 umol/mmol creatinineAbnormalAdolescent (13-18 years old)Female details
Xanthine (HMDB0000292) 6.8 umol/mmol creatinineAbnormalAdult (>18 years old)Male details
Displaying diseases 133 - 136 of 172 in total