Concentration Details

Metabolite
HMDB0000026 (Ureidopropionic acid)
Biospecimen
Cerebrospinal Fluid (CSF)
Status
Detected and Quantified
Data source
Referenced
Concentration
0.0 - 0.5 uM
Age
Children (1-13 years old)
Sex
Not Specified
Condition
Normal
References
    1. van Kuilenburg AB, Meijer J, Dobritzsch D, Meinsma R, Duran M, Lohkamp B, Zoetekouw L, Abeling NG, van Tinteren HL, Bosch AM: Clinical, biochemical and genetic findings in two siblings with a dihydropyrimidinase deficiency. Mol Genet Metab. 2007 Jun;91(2):157-64. Epub 2007 Mar 26. [PubMed:17383919 ]